CONGENITAL ABSENCE OF THE SPLEEN

A Case of Congenital Absence of the Spleen

Congenital malformations of the heart and the great vessels associated with congenital absence of the spleen.

The unusual combination of congenital malformations of the heart and great vessels on the one hand, with agenesis of the spleen on the other hand has been looked upon as a great medical curiosity. In the past it had been the pathologist exclusively who from time to time encountered this association of anomalies. More recently, however, cases have been diagnosed by the clinician during the life ...

Congenital Absence of Left Circumflex Coronary Artery

Congenital absence of left circumflex artery is a rare congenital anomaly of the coronary arteries. The prevalence of the anomaly in different studies ranges from 0.6% to 1.3%. Of these, 80% are benign and asymptomatic and 20% are clinically important. We report a 56-year-old man presented with acute resting chest pain who was diagnosed as having acute anterolateral infarction accompanied by el...

Clinical Implications of Congenital Absence of Circumflex Coronary Artery

Introduction: Coronary artery anomalies are rare clinical entities reported in 0.6% to 5.6% of diagnostic coronary angiographies. Anomalous origins of coronary arteries from distal segments are rarely reported. Presented herein is a coronary anomaly in which the circumflex artery (CX) originated as a continuation of the posterolateral branch of the right coronary artery (RCA) w...

Syndrome of Congenital Absence of the Spleen with Associated Cardiovascular and Gastroenteric Anomalies

Survey of 27 cases in the literature and the authors' 3 cases reveals a characteristic syndrome of congenital absence of the spleen with certain cardiovascular and gastrointestinal abnormalities. The hematologic and other findings permit a presumptive antemortem diagnosis. More accurate prognosis is made possible and valuable information is afforded the cardiac surgeon, since the cardiac anomal...